Langerhans Cell Histiocytosis: A Case Report

Om Shankar Chaurasiya, Ravi Ambey, Tarun Chandra


Langerhans cell histiocytosis (LCH) is a rare proliferative disorder in which pathological LC accumulate in a variety of organs. Historically the nomenclature regarding LCH has been confusing because the disease had been subcategorized simply based on different clinical manifestations. Herein, we report a child with classic fi nding of disseminated LCH, categorize and stratify on current recommendations of histiocyte society and discuss its treatment and prognosis.


Dendritic cells, Langerhans cells, Langerhans cell histiocytosis

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