Langerhans Cell Histiocytosis: A Case Report

Om Shankar Chaurasiya, Ravi Ambey, Tarun Chandra

Abstract


Langerhans cell histiocytosis (LCH) is a rare proliferative disorder in which pathological LC accumulate in a variety of organs. Historically the nomenclature regarding LCH has been confusing because the disease had been subcategorized simply based on different clinical manifestations. Herein, we report a child with classic fi nding of disseminated LCH, categorize and stratify on current recommendations of histiocyte society and discuss its treatment and prognosis.


Keywords


Dendritic cells, Langerhans cells, Langerhans cell histiocytosis

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